WDGMC Paediatric Liver Transplant Research Database
Date
2019-12-09
Authors
Fabian, June
Botha, Jean
Journal Title
Journal ISSN
Volume Title
Publisher
REDcap
Abstract
Biliary atresia (BA) is a progressive fibrosing cholangiopathy of infancy, the most common cause of cholestatic jaundice in infants and the top indication for liver transplantation in children. Kasai portoenterostomy (KPE) when successful may delay the requirement for liver transplantation, which in the majority offers the only cure. Good outcomes demand early surgical intervention, appropriate management of liver cirrhosis, and in most cases, liver transplantation. These parameters were audited of children with BA treated at the Steve Biko Academic Hospital (SBAH) in Pretoria, South Africa.
Description
All children with BA who were managed at SBAH between June 2007 and July 2018 were included. Parameters measured centered on patient demographics, timing of referral and surgical intervention, immediate and long-term outcomes of surgery, and follow-up management.
Keywords
Hepatic Transplantation
Citation
van der Schyff F, Terblanche Alberta J, Botha JF. Improving Poor Outcomes of Children With Biliary Atresia in South Africa by Early Referral to Centralized Units. JPGN. 2021; 2( 2): e073. DOI: 10.1097/PG9.0000000000000073