Retrospective review of right-sided hearts and associated cardiac malformations in children at the Chris Hani Baragwanath academic hospital
Date
2016-03-14
Authors
Van Staden, Nadia
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Abstract
Right-sided hearts have three different causes. They are often associated
with additional significant cardiac malformations (ASCM) and extracardiac
abnormalities.
Objectives
- To determine the prevalence of right-sided hearts.
- To distinguish between dextrocardia, dextroversion and dextroposition.
- To examine patient demographics.
- To examine ASCM and extracardiac abnormalities.
- To document patient management.
Methods
A retrospective audit of patient records.
Results
Dextrocardia comprised 1.8% of all congenital heart defects and 58% of all
right-sided hearts seen. Situs inversus was the dominant situs
arrangement. Situs solitus and situs ambiguous had a high incidence of
ASCM. Dextroposition made up 41% of all right-sided hearts and the
majority had causes amenable to treatment. Two patients were diagnosed
with dextroversion.
Conclusions
Dextrocardia as a cause of a right-sided heart shows no socioeconomic
or ethnic preference. ASCM are commonly seen in dextrocardia,
and depends largely on the situs arrangement. Dextroposition is mostly
secondary to extracardiac causes. Dextroversion is rare.
It is imperative to ascertain the cause of a right-sided heart, as this will
influence patient management and outcome.
Description
A research report submitted to the Faculty of Health Science, University of
the Witwatersrand, Johannesburg, in partial fulfillment of the requirements
for
the degree of Masters of Medicine in Paediatrics (MMed)
Johannesburg, 2014